Awareness of narcolepsy is low and screening tools needed. A total score above 14 is suggestive of narcolepsy with cataplexy. Swiss narcolepsy scale narcolepsy with cataplexy test. Disability benefits questionnaires list by dbq form name disability benefits questionnaires dbqs are medical examination forms used to capture essential information for evaluating disability compensation andor pension claims. Please choose the best answers using the scales shown for each question. Swiss narcolepsy scale snscataplexy with narcolepsy. It may occur with other symptoms such as cataplexy, sleep paralysis and hallucinations. Narcolepsy, too, is infrequently detected singh et al.
No side effects were reported, and the drug was welltolerated. See the finding a doctor section of this website for more information on finding a sleep specialist. Ullanlinna narcolepsy scale in diagnosis of narcolepsy. To validate the chinese version of ullanlinna narcolepsy scale cuns. The epworth sleepiness scale ess, the ullanlinna narcolepsy scale uns, and more recently the swiss narcolepsy scale. Created to assess individuals who may have narcolepsy with cataplexy. The finnish study suggested that the scale was very sensitive 100% and specific 98.
A 15item scale to assess the frequency and severity of excessive daytime sleepiness, cataplexy, hypnagogic hallucinations, sleep paralysis, and disrupted nighttime sleep was developed and validated. This page lists resources of potential interest for people seeking to learn more about narcolepsy. A positive result supports a diagnosis, but does not make it 100% certain 30% of people without narcolepsy also have the genetic marker. Using the sns, a validated tool for screening for narcolepsy with cataplexy. However, in almost 10% of the cases, patients with narcolepsy along with muscle weakness have close relatives suffering from this condition 1 actigraphy.
Print out the ullanlinna narcolepsy scale pdf to assess your symptoms. Get the doctor discussion guide now or download the pdf. However, one of the major limitations of the scale is that it may only detect the severe cases of narcolepsy and may miss some of the milder cases or cases who are developing narcolepsy. The ullanlinna narcolepsy scale named after the clinic in finland where it was developed is also a wellvalidated questionnaire for diagnosing narcolepsy with cataplexy.
For example, 80 to 90 percent of obstructive sleep apnea osa cases remain undiagnosed and untreated, which increases the burden of this disorder kapur et al. The epworth sleepiness scale can be used to assess daytime sleepiness. Boshes professor in neurology professor of neurobiology director center for circadian and sleep medicine director sleep disorders center northwestern university feinberg school of medicine solomon a. Hence, there is a need for narcolepsy medications with novel mechanisms of action that are associated with minimal or no abuse potential. Safety and efficacy of pitolisant on cataplexy in patients. Exploring symptoms in adults swiss narcolepsy scale sns the sns helps determine if you may have narcolepsy with cataplexy. A validity study of ullanlinna narcolepsy scale in hong. We also show that if ullanlinna narcolepsy scale score is less than 9, narcolepsy is highly unlikely. Narcolepsy is often linked to a deficiency in the sleepregulating brain chemical hypocretin, also known as orexin.
Nevertheless, this scale can be used as a simple and reliable screening tool to estimate the prevalence of narcolepsy cataplexy in the general population. We show that ullanlinna narcolepsy scale has excellent sensitivity and specificity in the screening of narcolepsy type 1 in a clinical population. Total scores can range from 0 to 44 with higher scores denoting greater narcoleptic tendencies. Study objectives to validate ullanlinna narcolepsy scale uns as a screening tool for narcolepsy in a clinical population and to compare it with swiss narcolepsy scale sns and epworth. Evaluation of the abuse potential of pitolisant, a. Download a pdf of your results to share at your next appointment, or email. Narcolepsy is a chronic neurological sleep disorder, the diagnosis of which is based upon clinical evaluation and additional paraclinical assessments. Complete this and share your results with your healthcare provider. This fiveitem scale was found to have high sensitivity 96% and specificity 98% for the diagnosis. This tool has been shown to have high specificity and.
The swiss narcolepsy scale sns helps determine if you may have narcolepsy with cataplexy. In these episodes a person suddenly falls asleep in unusual situations, such as. The swiss narcolepsy scale was found to have the best. Scale in those with narcolepsy tend to reflect moderate to severe sleepiness, or at least, as opposed to patients with obstructive sleep apnea, whose scores commonly reflect milder sleepiness. This quiz is designed to help you recognize if you potentially have narcolepsy. Narcolepsy is a neurological sleep disorder that causes a potentially disabling level of daytime sleepiness. Please circle the number that best describes each situation. When laughing, feeling glad or angry, or in an exciting situation, have the following symptoms suddenly occurred. Swiss narcolepsy scale sns kit order form thank you for your interest in the swiss narcolepsy scale sns the sns is designed to screen for narcolepsy with cataplexy in patients with excessive daytime sleepiness. How likely are you to doze off or fall asleep during the following situations, in contrast to just feeling tired. The most popular abbreviation for ullanlinna narcolepsy scale is.
Pitolisant is a firstinclass medication for the treatment of narcolepsy, with a novel mechanism of action 21, 22. The ullanlinna narcolepsy scale uns was developed by hublin et al. However, as suggested by the authors, this simple but very useful questionnaire needed to be replicated and validated in other ethnic populations,14. How likely are you to dose off or fall asleep in the situation described below, in contrast to feeling just tired. If you suspect you have narcolepsy, discuss your concerns with a medical professional familiar with narcolepsy and other sleep disorders. Narcolepsy is a longterm neurological disorder that involves a decreased ability to regulate sleepwake cycles. To validate the narcolepsy severity scale nss, a brief clinical instrument to evaluate the severity and consequences of symptoms in patients with narcolepsy type 1 nt1.
Epworth sleepiness scale and swiss narcolepsy scale. Narcolepsy uk exists for the benefit, relief and aid of persons suffering from narcolepsy. Narcolepsy is a chronic neurological disorder of excessive daytime sleepiness. Symptoms often include periods of excessive daytime sleepiness and brief involuntary sleep episodes. This sleepiness may occur in the form of repeated and irresistible sleep attacks. Summary the ullanlinna narcolepsy scale uns is a simple questionnaire. In a previous study, 10 we reported the accuracy of a new scale the swiss narcolepsy scale sns for the diagnosis of narcolepsy in 57 patients with narcolepsy when compared with 40 controls and 56 patients with eds. Epworth sleepiness scale ess and swiss narcolepsy scale. Harvard medical schools division of sleep medicine and its sleep and health education program assume no responsibility for content on external sites, nor does listing here indicate any editorial endorsement or approval of the content of these sites. These free educational resources are provided to help you learn more about narcolepsy and its symptoms, and to help you discuss your symptoms with a sleep specialist. Methods study design and participants we did a randomised, doubleblind, placebocontrolled trial with patients recruited from 16 sleep centres referred by a local doctor in nine countries bulgaria, czech republic, hungary, macedonia, poland, russia, serbia. All people with narcolepsy have excessive drowsiness. These materials are intended for us residents 18 years of age or older and are not intended to replace a conversation with a sleep specialist. Sleep records are generated for the patient who complains of excessive day time sleep.
The uns is an 11item questionnaire that assesses eds and cataplexy, with 7. The uns is an 11item scale designed to evaluate a variety of symptoms relating to narcolepsy, including frequency of daytime narcoleptic episodes, muscle weakness associated with powerful emotions, and nighttime sleep latency. The 11item scale range 044 assesses the two main features of the narcoleptic syndrome, the abnormal sleeping tendency and cataplexy. It is a fiveitem patient reported scale that assesses the frequency of five symptoms that can be used to screen for the presence of narcolepsy with cataplexy. Patients with narcolepsy usually score 18 range 1420 out of a possible 24 points on the nonspecific epworth sleepiness scale 33,34,250. Often less than once a month times a month 12 times a week q2.
These experiences can be brought on by strong emotions. For other ways to identify problematic sleepiness, see selfevaluation daytime sleepiness can have many causes, including narcolepsy, which affects up to 1 in 2,000 people. For patients who score 10 on the epworth sleepiness scale, consider using the swiss narcolepsy scale sns. About 70% of those affected also experience episodes of sudden loss of muscle strength, known as cataplexy.
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